International Journal of Head and Neck Surgery

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VOLUME 11 , ISSUE 2 ( April-June, 2020 ) > List of Articles


Surgical Management of Unilateral Craniosynostosis: A Case Report

Munaza Shafi, Mohammad Shakeel, Mudasar Ahad, Imran Ahmed

Keywords : Fronto-orbital advancement, Plagiocephaly, Unilateral craniosynostosis

Citation Information : Shafi M, Shakeel M, Ahad M, Ahmed I. Surgical Management of Unilateral Craniosynostosis: A Case Report. Int J Head Neck Surg 2020; 11 (2):39-41.

DOI: 10.5005/jp-journals-10001-1346

License: CC BY-NC 4.0

Published Online: 01-04-2020

Copyright Statement:  Copyright © 2020; The Author(s).


Craniosynostosis is the premature fusion of cranial sutures which can result in neurological abnormalities, facial and skull deformations, and increased intracranial pressure. It can be diagnosed by physical examination, the use of plain film X-rays, computed tomography (CT) exams, or with the use of ultrasound. If caught within the first few months of life, or prenatally, craniosynostosis can be treated endoscopically with minimal invasiveness. Those cases that are discovered after the first 6 months of life can be treated surgically with cranial vault remodeling. Both procedures have an excellent success rate and a low recurrence rate. In this case report, a 6-month-old healthy boy with deformity of the left forehead and orbit that is caused by frontal plagiocephaly and coronal unilateral synostosis is presented. This abnormality was corrected by frontal craniotomy and fronto-orbital complex advancement under general anesthesia.

  1. Bell WH. Modern practice in orthognatic and reconstructive surgery, 1st ed. Dallas: WB Saunders Co; 1992. pp. 1845–1854.
  2. Francel PC, Park TS, et al. Frontal plagiocephly secondary to synop-sis of the frontosphenoidal suture. Case report. J Neurosurg 1995 Oct;83(4):733–736. DOI: 10.3171/jns.1995.83.4.0733.
  3. Bruneteau RJ, Mulliken JB. Frontal plagio-cephaly: synostotic, compensational, or de-formational. Plast Reconstr Surg 1992 Jan;89(1):21–31. DOI: 10.1097/00006534-199289010-00005.
  4. de Ribaupierre S, Czorny A, et al. Frontosphenoidal synostosis: a rare cause of unilateral anterior plagiocephaly. Childs Nerv Syst 2007 Dec;23(12):1431–1438. DOI: 10.1007/s00381-007-0469-4.
  5. Davutoglu M, Okur N, et al. Craniosynostosis associated with lacunar skull: three-dimensional computed tomography features. Eur J Gen Med 2010;7(1):104–106. DOI: 10.29333/ejgm/82829.
  6. Rogers GF, Proctor MR, et al. Uni-lateral fusion of the frontosphenoidal suture: a rare cause of synostotic frontal plagiocephaly. Plast Reconstr Surg 2002 Sep;110(4):1011–1015. DOI: 10.1097/01.PRS.0000021308.37931.18.
  7. Schmidek A, Sweet WH. Operative neuro-surgical techniques, indications, methods and results, 4th ed. Philadelphia: WB Saunders Co; 2000. pp. 126–128.
  8. Khanna P, Thapa M, et al. Pictorial essay: the many faces of craniosynostosis. Indian J Radiol 2011;21(1):1–9. DOI: 10.4103/0971-3026.76055.
  9. Sun PP, Persing JA. Craniosynostosis. In: Albright AL, Pollack IF, Adelson PD. ed. Principles and practice of pediatric neurosurgery. New York: Thieme Medical; 1999. pp. 219–242.
  10. Aviv RI, Rodger E, et al. Craniosynostosis. Clin Radiol 2002;57:93–102. DOI: 10.1053/crad.2001.0836.
  11. Ghali GE, Sinn DP, et al. Management of nonsyndromic craniosynostosis. Atlas Oral Maxillofac Surg Clin North Am 2002;10:1–41. DOI: 10.1016/S1061-3315(01)00003-8.
  12. Zoller JE, Kubler AC, et al. Kraniozynostosen. In: Zoller JE, Kubler AC. ed. Kraniofaziale chirurgie. Stuttgart: Thieme; 2002. Chapter 2.
  13. Dundulis JA, Becker DB, et al. Coronal ring involve-ment in patients treated for unilateral coronal craniosynostosis. Plast Reconstr Surg 2004 Dec;114(7):1695–1703. DOI: 10.1097/01.PRS.0000142474.25114.CB.
  14. Cohen Jr MM. The etiology of craniosynostosis. In: Cohen Jr MM. ed. Craniosynostosis: Diagnosis, Evaluation and Management. New York: Raven Press; 1986. pp. 65–66.
  15. Glass IA, Chapman S, et al. A distinct autosomal dominant craniosynostosis-brachydactyly syndrome. Clin Dysmorphol 1994;3:215–223. DOI: 10.1097/00019605-199407000-00005.
  16. Muenke M., Gripp KW, et al. A unique point mutation in the fibroblast growth factor receptor 3 gene (FGFR3) defines a new craniosynostosis syndrome. Am J Hum Genet 1997;60:555–564.
  17. Marsh JL, Gado MH, et al. Osseous anatomy of unilateral coronal synostosis. Cleft Palate J 1986;23:87–100.
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