International Journal of Head and Neck Surgery

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VOLUME 12 , ISSUE 2 ( April-June, 2021 ) > List of Articles


Lhermitte–Duclos Disease: Case Report and Literature Review

Brajesh Kumar, Samrendra Kumar Singh, Om Prakash Gupta, KM Jha

Keywords : Dysplastic gangliocytoma, Headache, Lhermitte–Duclos disease

Citation Information : Kumar B, Singh SK, Gupta OP, Jha K. Lhermitte–Duclos Disease: Case Report and Literature Review. Int J Head Neck Surg 2021; 12 (2):65-70.

DOI: 10.5005/jp-journals-10001-1424

License: CC BY-NC 4.0

Published Online: 01-06-2021

Copyright Statement:  Copyright © 2021; The Author(s).


Lhermitte–Duclos disease (LDD) is a neurological disorder caused by a hamartomatous lesion within the cerebellum. Clinically, LDD is often associated with symptoms of the space-occupying lesion due to increased intracranial pressure, hydrocephalus, and focal neurological deficit. This was a case of a 36-year-old woman who presented with progressive headache and difficulty in swallowing liquids. Magnetic resonance imaging demonstrated a right cerebellar mass lesion with the characteristic “tiger-striped appearance”. There was an inferior displacement of the right cerebellar tonsil. She underwent ventriculoperitoneal (VP) shunt and followed by partial resection of the tumor to decrease the mass effect. Her headache gradually improved and she was able to swallow liquids by the time of discharge.

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