Lhermitte–Duclos disease (LDD) is a neurological disorder caused by a hamartomatous lesion within the cerebellum. Clinically, LDD is often associated with symptoms of the space-occupying lesion due to increased intracranial pressure, hydrocephalus, and focal neurological deficit. This was a case of a 36-year-old woman who presented with progressive headache and difficulty in swallowing liquids. Magnetic resonance imaging demonstrated a right cerebellar mass lesion with the characteristic “tiger-striped appearance”. There was an inferior displacement of the right cerebellar tonsil. She underwent ventriculoperitoneal (VP) shunt and followed by partial resection of the tumor to decrease the mass effect. Her headache gradually improved and she was able to swallow liquids by the time of discharge.
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