International Journal of Head and Neck Surgery

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VOLUME 9 , ISSUE 4 ( October-December, 2018 ) > List of Articles

CASE REPORT

Synechiae of the Oral Cavity with Cleft Palate: A Rare Congenital Anomaly

Hitendra Prakash Singh, Sunil Kumar, Neha Rautela, Meraj Ahmad

Keywords : Oral synechiae, Orofacial anomalies, Syngnathia,Maxillo-mandibular fusion

Citation Information : Singh HP, Kumar S, Rautela N, Ahmad M. Synechiae of the Oral Cavity with Cleft Palate: A Rare Congenital Anomaly. Int J Head Neck Surg 2018; 9 (4):128-130.

DOI: 10.5005/jp-journals-10001-1359

License: CC BY-NC 4.0

Published Online: 00-12-2018

Copyright Statement:  Copyright © 2018; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Aim: Fusion defects of maxilla and mandible are a rare congenital anomaly that affect the growth and development of patients in varying extents. Authors intend to present a case of incomplete synechiae of the oral cavity. Background: Congenital maxillo-mandibular fusions present with varying degree of involvement of mucosa, soft tissues and bone and can cause aerodigestive problems in the neonatal period. Case description: A 5-day-old male child was referred from pediatrics for evaluation for complaints of inability to feed. On examination, a mucosal band was noted connecting the floor of the mouth with the hard palate, with free margins on both sides. After proper consent, the mucosal band was completely excised under local anesthesia and hemostasis was achieved. The rest of the oral cavity and oropharynx was normal except cleft palate. Conclusion: These types of anomalies have to be diagnosed as early as possible in the early neonatal life. Early diagnosis and appropriate management should be instituted to prevent risks of asphyxia, aspiration pneumonitis, growth retardation, malnutrition, facial growth abnormalities, and improper eruption of teeth. Clinical significance: As there are various types of presentations, the treatment needs to be individualized.


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  1. Mortazavi SH, Motamedi MH. Congenital fusion of the jaws. Indian J Pediatr 2007;74:4168. DOI: 10.1007/s12098-007-0071-5.
  2. Mir MA, Iqbal S, et al. Syngnathia without any other associated anomaly very rare case report. Internet J Plast Surg 2007;4:1.
  3. Tanrikulu R, Erol B, et al. Congenital alveolar synechiae: a case report. Br Dent J 2005;198:81–82. DOI: 10.1038/sj.bdj.4811971.
  4. Dawson KH, Gruss JS, et al. Congenital bony syngnathia: a proposed classification. Cleft Palate Craniofac J 1997;34:141–146. DOI: 10.1597/1545-1569_1997_034_0141_cbsapc_2.3.co_2.
  5. Laster Z, Temkin D, et al. Complete bony fusion of the mandible to the zygomatic complex and maxillary tuberosity: case report and review. Int J Oral Maxillofac Surg 2001;30:75–79. DOI: 10.1054/ijom. 2000.0009.
  6. Verloesa A, Raoula M, et al. Bony syngnathia, vertebral segmentation defect, coloboma, microcephaly and mental retardation: confirmation of Dobrow syndrome and review of syndromal syngnathias. Clin Dysmorphol 2004;13:205–211. DOI: 10.1097/00019605-200410000-00002.
  7. Parkins GE, Boamah MO. Congenital maxillomandibular syngnathia: Case report. J Craniomaxillofac Surg 2009;37:2768. DOI: 10.1016/j.jcms.2009.01.001.
  8. Shams MG, Motamedi MH, et al. Congenital fusion of the maxilla and mandible: Brief case report. Oral Surg Oral Med Oral Pathol Oral Radiol Endod 2006;102:e13. DOI: 10.1016/j.tripleo.2005.10.051.
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