Klippel–Trenaunay Syndrome with Hearing Loss: Is it the Cause? A Rare Case Report
Trilok C Guleria, Mahender Singh, Ramesh Azad, Narender K Mohindroo
Keywords :
Case report, Hemangiomatous, Nevus, Osteohypertrophique, Tranuanay, Variqueux
Citation Information :
Guleria TC, Singh M, Azad R, Mohindroo NK. Klippel–Trenaunay Syndrome with Hearing Loss: Is it the Cause? A Rare Case Report. Int J Head Neck Surg 2023; 14 (3):59-61.
Two French physicians, Maurice Klippel and Paul Trenaunay, described two patients with hemangiomatous lesions of the skin and coined the term “nevus variqueux osteohypertrophique.” Klippel–Trénaunay syndrome (KTS) is characterized by a triad of capillary malformations, venous malformations, and soft tissue or bony hypertrophy. The etiology of the syndrome is unknown. Diagnosis of KTS is mainly clinical. An appropriate multidisciplinary approach to treatment and prevention of possible complications of KTS provides optimal care for the patient. KTS with hearing loss is a very rare presentation. We describe a case report of KTS in a 5-year-old boy associated with bilateral conductive hearing loss.
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